Myeloma-associated Systemic Amyloidosis with an Extensive Cutaneous Involvement
نویسندگان
چکیده
Primary systemic amyloidosis (PSA) mostly occurs in the setting of plasma cell dyscrasias.[1] It is difficult to diagnose as it usually presents with nonspecific symptoms.[2] Mucocutaneous manifestations occur in 29%–40% of cases and provide important diagnostic clues.[3] We report an atypical case where an unusually extensive cutaneous involvement provided the first sign of a widespread multiorgan infiltration by amyloid protein and eventually led to the diagnosis of multiple myeloma.
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